Moaçir Wajner

Research interests

Publications

• Mitochondrial dysfunction in fatty acid oxidation disorders: insights from human and animal studies

  Bioscience Reports · 2015 · https://doi.org/10.1042/bsr20150240

• l-carnitine supplementation as a potential antioxidant therapy for inherited neurometabolic disorders

  Gene · 2013 · https://doi.org/10.1016/j.gene.2013.10.017

• Resveratrol Protects C6 Astrocyte Cell Line against Hydrogen Peroxide-Induced Oxidative Stress through Heme Oxygenase 1

  PLoS ONE · 2013 · https://doi.org/10.1371/journal.pone.0064372

• An overview of L-2-hydroxyglutarate dehydrogenase gene (L2HGDH) variants: a genotype-phenotype study

  Human Mutation · 2010 · https://doi.org/10.1002/humu.21197

• α-Ketoisocaproic acid and leucine provoke mitochondrial bioenergetic dysfunction in rat brain

  Brain Research · 2010 · https://doi.org/10.1016/j.brainres.2010.02.018

• l -2-Hydroxyglutaric Aciduria: Pattern of MR Imaging Abnormalities in 56 Patients

  Radiology · 2009 · https://doi.org/10.1148/radiol.2513080647

• Natural History, Outcome, and Treatment Efficacy in Children and Adults with Glutaryl-CoA Dehydrogenase Deficiency

  Pediatric Research · 2006 · https://doi.org/10.1203/01.pdr.0000219387.79887.86

• In vitro evidence for an antioxidant role of 3-hydroxykynurenine and 3-hydroxyanthranilic acid in the brain

  Neurochemistry International · 2006 · https://doi.org/10.1016/j.neuint.2006.04.017

• Oxidative stress in patients with phenylketonuria

  Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease · 2005 · https://doi.org/10.1016/j.bbadis.2005.02.005

• The role of oxidative damage in the neuropathology of organic acidurias: Insights from animal studies

  Journal of Inherited Metabolic Disease · 2004 · https://doi.org/10.1023/b:boli.0000037353.13085.e2

• Evidence that oxidative stress is increased in patients with X-linked adrenoleukodystrophy

  Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease · 2003 · https://doi.org/10.1016/j.bbadis.2003.10.004

• D‐2‐hydroxyglutaric acid induces oxidative stress in cerebral cortex of young rats

  European Journal of Neuroscience · 2003 · https://doi.org/10.1046/j.1460-9568.2003.02639.x

• Inhibition of the mitochondrial respiratory chain complex activities in rat cerebral cortex by methylmalonic acid

  Neurochemistry International · 2002 · https://doi.org/10.1016/s0197-0186(01)00130-9

• Reduction of Na+,K+-ATPase Activity in Hippocampus of Rats Subjected to Chemically Induced Hyperhomocysteinemia

  Neurochemical Research · 2002 · https://doi.org/10.1023/a:1021670607647

• Guanosine Enhances Glutamate Uptake in Brain Cortical Slices at Normal and Excitotoxic Conditions

  Cellular and Molecular Neurobiology · 2002 · https://doi.org/10.1023/a:1020728203682

• Inhibition of Na+,K+-ATPase Activity in Hippocampus of Rats Subjected to Acute Administration of Homocysteine Is Prevented by Vitamins E and C Treatment

  Neurochemical Research · 2002 · https://doi.org/10.1023/a:1021647329937

• Quinolinic acid inhibits glutamate uptake into synaptic vesicles from rat brain

  Neuroreport · 2000 · https://doi.org/10.1097/00001756-200002070-00005

• Propionic and L-methylmalonic acids induce oxidative stress in brain of young rats

  Neuroreport · 2000 · https://doi.org/10.1097/00001756-200002280-00023

• Methylmalonate administration decreases Na+,K+-ATPase activity in cerebral cortex of rats

  Neuroreport · 2000 · https://doi.org/10.1097/00001756-200007140-00052

• Selective screening of 10,000 high-risk Brazilian patients for the detection of inborn errors of metabolism

  European Journal of Pediatrics · 1997 · https://doi.org/10.1007/s004310050685

• Distribution of xanthine dehydrogenase and oxidase activities in human and rabbit tissues

  Biochimica et Biophysica Acta (BBA) - General Subjects · 1989 · https://doi.org/10.1016/0304-4165(89)90031-7

Current projects

No projects listed.